This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

H. B. Perlman, MD

Arch Otolaryngol. 1969;90(2):232-234.

	Since this article does not have an abstract, we have provided the first 150 words of the full text PDF and any section headings.

A NUMBER of articles dealing with familial nerve deafness have added to the previously published reports of this irreversible and often progressive affliction.

Mengel et al¹ state that only nine of 54 types of hereditary nerve deafness have no associated abnormalities. In the sex linked are congenital, severe, early onset, high tone deafness; in the dominant are midfrequency, progressive and unilateral deafness. Finally a recessive congenital severe deafness is recognized. They propose another recessive type (recessive, early onset, neural deafness) on the basis of their study of a Mennonite family with 16 deaf members. History, sonograms, and auditory tests suggest some hearing in early childhood that deteriorates by late childhood.

Proctor and Proctor² present a useful classification of dominant and recessive nerve deafness associated with a wide variety of hereditary disease. They point out that the pathological changes are usually confined to the organ of Corti and stria . . . [Full Text PDF of this Article]

Author Affiliations
Chicago

From the Department of Surgery (Otolaryngology) of the University of Chicago.

Footnotes
Accepted for publication Oct 28, 1968.

Reprint requests to Department of Surgery (Otolaryngology), University of Chicago, 950 E 59th St, Chicago 60637.

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?