This Article  • Full text  • PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Contact me when this article is cited  Related Content  • Related article  • Similar articles in this journal  Topic Collections  • Neurology  • Neurocutaneous Diseases  • Oncology  • Head & Neck Cancer  • Neoplasms of Head & Neck  • Alert me on articles by topic

Anil K. Lalwani, MD

Arch Otolaryngol Head Neck Surg. 2007;133(9):857.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

JAMA

Mechanisms of Morbid Hearing Loss Associated With Tumors of the Endolymphatic Sac in von Hippel-Lindau Disease 

John A. Butman, MD, PhD; H. Jeffrey Kim, MD; Martin Baggenstos, MD; Joshua M. Ammerman, MD; James Dambrosia, PhD; Athos Patsalides, MD; Nicholas J. Patronas, MD; Edward H. Oldfield, MD; Russell R. Lonser, MD

Context:  Endolymphatic sac tumors (ELSTs) are associated with von Hippel-Lindau disease and cause irreversible sensorineural hearing loss (SNHL) and vestibulopathy. The underlying mechanisms of audiovestibular morbidity remain unclear, and optimal timing of treatment is not known.

Objective:  To define the underlying audiovestibular pathophysiologic mechanisms associated with ELSTs.

Design, Setting, and Patients:  Prospective and serial evaluation of patients with von Hippel-Lindau disease and ELSTs at the National Institutes of Health between May 1990 and December 2006.

Main Outcome Measures:  Clinical findings and audiologic data were correlated with serial magnetic resonance imaging and . . . [Full Text of this Article]