This Article  • Full text  • PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Topic Collections  • Radiology of Head & Neck  • Alert me on articles by topic  Social Bookmarking   What's this?

Arch Otolaryngol Head Neck Surg. 2005;131:536-537.

	Since this article does not have an abstract, we have provided the first 150 words of the full text and any section headings.

Diagnosis: Autoimmune inner ear disease (AIED)

Although McCabe¹ first reported AIED in adults in 1979, little is known about the diagnosis and management of AIED in the pediatric population. The differential diagnosis of our patient’s hearing loss included juvenile rheumatoid arthritis with inner ear involvement, atypical Cogan syndrome, systemic lupus erythematosus, relapsing polychondritis, Behçet syndrome, Wegener granulomatosis, polyarteritis nodosa, and the more rare Vogt-Koyanagi-Harada syndrome (uveoencephalitis that includes decreased visual acuity, meningitis signs, SNHL, and poliosis or alopecia).² In the present case, because of the patient’s age, most of these causes of SNHL were unlikely. When AIED is being considered as a possible cause, the main features include rapidly progressive bilateral hearing loss due to either systemic or organ-specific disease when there is reactivity against a self-antigen found in the inner ear.³ Ndiaye et al² reported 3 cases of pediatric Cogan syndrome that share some features with our case, such as ophthalmologic and rheumatologic involvement with . . . [Full Text of this Article]

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?