This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Citing articles on HighWire  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

Kristi Adachi, MD; Richard A. Chole, MD, PhD

Arch Otolaryngol Head Neck Surg. 1990;116(10):1205-1207.

Abstract
• Hurler syndrome is a rare mucopolysaccharide storage disease that becomes clinically apparent during early childhood as mucopolysaccharide deposits form in skeletal and soft tissues. Progressive mucopolysaccharide deposition in the oropharynx and tracheal connective tissues leads to airway obstruction if untreated. Tonsillectomy, adenoidectomy, and tracheostomy have been utilized to provide symptomatic relief of upper airway obstruction. Treatment of tracheal lesions by laser excision is a recent innovative method for the management of airway obstruction in children with Hurler syndrome. We describe two boys with Hurler syndrome whose mucopolysaccharide tracheal lesions were excised by utilization of the carbon dioxide laser.

(Arch Otolaryngol Head Neck Surg. 1990;116:1205-1207)

Author Affiliations
From the Department of Otolaryngology, University of California, Davis School of Medicine.

Footnotes
Accepted for publication December 17, 1989.

Reprint requests to University of California, Davis, Otology Research Laboratory, 1159 Surge III, Davis, CA 95616 (Dr Chole).

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?

THIS ARTICLE HAS BEEN CITED BY OTHER ARTICLES

Airway Management in Children With Mucopolysaccharidoses
Yeung et al.
Arch Otolaryngol Head Neck Surg 2009;135:73-79.
ABSTRACT | FULL TEXT