Congenital cholesteatoma of the petrous pyramid
K. L. Horn, J. J. Shea 3rd and D. E. Brackmann
A 20-year follow-up was done on a patient with a large congenital
cholesteatoma of the petrous apex. The patient was treated successfully
with marsupialization through a radical mastoidectomy and sphenoid
sinusotomy. Cranial computed tomography and magnetic resonance imaging
demonstrated continued cholesteatoma growth. Bone-conduction thresholds
remained normal despite replacement of the internal auditory canal by
cholesteatoma matrix. The patient continues to have chronic otorrhea, but
is otherwise asymptomatic.
