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Facioscapulohumeral Muscular Dystrophy and Accompanying Hearing Loss
Marion D. Meyerson, PhD;
Ernest Lewis, MA;
Karen, Ill, MS
Arch Otolaryngol. 1984;110(4):261-266.
Abstract
• Facioscapulohumeral (FSH) muscular dystrophy (MD) is an autosomal dominant condition marked by muscle weakness primarily in the face, shoulder girdle, and legs. Intelligence and life span are normal and the spectrum of disability is broad. Flaccid dysarthria results from the facial muscle paralysis. A pair of siblings had FSH MD that was accompanied by the unusual finding of sensorineural hearing loss. Speech and audiologic aspects are presented and etiologic explanations are suggested. Careful audiologic evaluation of all patients with FSH MD is advised so that sensorineural hearing loss can be ruled out.
(Arch Otolaryngol 1984;110:261-266)
Author Affiliations
From the San Francisco Hearing and Speech Center (Dr Meyerson, Mr Lewis, and Ms Ill); and San Francisco State and San Jose State universities (Dr Meyerson).
Footnotes
Accepted for publication April 28, 1983.
Reprint requests to San Francisco Hearing and Speech Center, 1234 Divisadero St, San Francisco, CA 94115 (Dr Meyerson).
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