This Article  • References  • Full text PDF  • Reply to article  • Send to a friend  • Save in My Folder  • Save to citation manager  • Permissions  Citing Articles  • Citing articles on HighWire  • Contact me when this article is cited  Related Content  • Similar articles in this journal  Social Bookmarking   What's this?

Cor W. R. J. Cremers, MD; Gerrit A. Hoogland, MD; Wim Kuypers, PhD

Arch Otolaryngol. 1984;110(1):54-57.

Abstract
• A 22-year-old woman with mixed hearing loss, Klippel-Feil anomalad (fused cervical vertebrae), and bilateral abducens palsy with retracted bulb (Duane's syndrome) is classified as having the cervico-oculo-acoustic syndrome or Wildervanck syndrome. In this syndrome, the unilateral or bilateral congenital hearing loss is usually severe and of neurosensory origin. To our knowledge, this is the third case of this syndrome with the classical triad and a mixed hearing loss. It is the second case in which an exploratory tympanotomy was performed. An ankylosis of the stapes was found. Stapedectomy and Teflon interposition were successfully carried out. Since the triad of the cervico-oculo-acoustic syndrome can be incomplete, a review of the association of Klippel-Feil anomalad and hearing loss is also presented, with special attention to the anomalies of the ossicular chain.

(Arch Otolaryngol 1984;110:54-57)

Author Affiliations
From the Department of Otorhinolaryngology, St Radboud Hospital, University of Nijmegen, the Netherlands.

Footnotes
Accepted for publication Dec 10, 1982.

Reprint requests to Department of Otorhinolaryngology, St Radboud Hospital, University of Nijmegen, the Netherlands. (Dr Cremers).

CiteULike    Connotea    Del.icio.us    Digg    Reddit    Technorati    Twitter     What's this?

THIS ARTICLE HAS BEEN CITED BY OTHER ARTICLES

Proximal Symphalangia and Stapes Ankylosis
Cremers et al.
Arch Otolaryngol Head Neck Surg 1985;111:765-767.
ABSTRACT