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A Temporal Bone Report

Andrew W. Miglets, MD; David Schuller, MD; Elizabeth Ruppert, MD; David J. Lim, MD

Arch Otolaryngol. 1975;101(7):433-437.

Abstract
Since Edwards first described the trisomy 17-18 syndrome in 1960, the findings in the temporal bones of only four patients with this condition have been reported. They varied widely, ranging from a normal temporal bone, to severe malformations of both the middle and inner ear structures.

This study describes the temporal bone findings in a patient with this syndrome. Many of the abnormalities described previously were present as well as the following unreported findings: complete bony atresia of the external canal, an aberrant tensor tympani muscle that did not insert into the malleus but rather attached to a dehiscent area in the Fallopian canal, wide short utricular and saccular ducts, and a widely patent cochlear aqueduct. There was also a developmental arrest of the membranous structures within the cochlea that probably occurred during the 12th week of fetal life.

Author Affiliations
From the departments of otolaryngology and pediatrics of the Ohio State University Hospitals, Columbus.

Footnotes
Accepted for publication Feb 25, 1975.

Reprint requests to 456 Clinic Dr, Room 3118, Columbus, OH 43210 (Dr. Miglets).

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